Consanguinity and complex cardiac anomalies with situs ambiguus.
نویسندگان
چکیده
منابع مشابه
The cardiac conduction system in situs ambiguus.
The cardiac specialized conduction tissue was studied by serial sectioning in 13 cases of situs ambiguus. In four cases of right isomerism, we found paired sinus nodes in relation to a crista terminalis, and in each case a sling of conduction tissue between two atrioventricular nodes was present regardless of the ventricular morphology or cardiac position. In the cases with left isomerism, the ...
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Primary ciliary dyskinesia (PCD) is a rare disorder with impaired ciliary function resulting in a spectrum of clinical manifestations of varying severity. PCD affects approximately one in every 20,000 individuals with a reported prevalence between 1:4000 and 1:50,000. Due to its nonspecific clinical features, the condition is usually diagnosed late in its course, unless situs inversus (SI) or o...
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The first case of mitral stenosis in a patient with situs inversus was reported from this hospital in 1911 (Owen). We have found four reports of mitral valvotomy in such cases (Berkowitz and Likoff, 1954; Koshy et al., 1955; Naef, 1957; Michaud et al., 1959) and a fifth is reported here. Viscott (1960) collected some 900 previously reported cases of complete situs inversus and suggested that it...
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PURPOSE To describe the perioperative assessment and anaesthetic management for surgical separation of three sets of conjoined twins with complex cardiac anomalies threatened with arterial desaturation and haemodynamic instability. CLINICAL FEATURES Three sets of conjoined twins, one omphaloischiopagus, one omphalopagus, and one thoraco-omphalopagus, were considered for separation during the ...
متن کاملPartial situs inversus with levocardia. An unusual combination of anomalies.
AN INSTANCE of a unique combinationi 1A . of anomnalies was recently encountered in ani inifant with eyanotic congenital heart disease who died at the age of 13 months. The clinical course and pathologic finding,s are described. Case History The patient was a femiiale baby, born at full terim after ani uneventful pregnancy. At birth she weighed 6 lbs. and was eyanotic. Heart disease was first d...
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ژورنال
عنوان ژورنال: Archives of Disease in Childhood
سال: 1984
ISSN: 0003-9888,1468-2044
DOI: 10.1136/adc.59.3.242